Bénédicte Neven

Also affiliated with Hôpital Necker-Enfants Malades, Inserm, Université Paris Cité, Assistance Publique – Hôpitaux de Paris, Center for Rheumatology, Institut des Maladies Génétiques Imagine

Immunology and MicrobiologyMedicineBiochemistry, Genetics and Molecular Biology

Pilot corpus only

This score is computed over theSindex pilot corpus and does not cover the full scientific literature. Scores are relative to papers we have ingested — papers, authors, and institutions outside the pilot are not represented. Methodology.

Top 2%percentile

2.3Author DataRank

Indexed papers

2in pilot corpus

datarank_citation_only_1hop_v6· scope data_onlyMethodology

Why this DataRank?

An author's DataRank is the sum of the DataRanks of all 2 indexed papers attributed to them. A prolific author with many moderate-impact papers can outrank one with a single high-impact paper.

Author scores recompute whenever paper DataRanks are refreshed, so this number lags the underlying paper scores by at most one batch run.

Read the full methodology →

The highest-impact dataset this researcher has shared, ranked by DataRank — the single contribution doing the most to lift their data-sharing standing.

International retrospective study of allogeneic hematopoietic cell transplantation for activated PI3K-delta syndrome

Journal of Allergy and Clinical Immunology(2021)10.1016/j.jaci.2021.04.036

Top 9%

2.3DataRank

Top 9%72 citations

Zohreh Nademi, Maria Elena Maccari, Stephan Ehl, Gülbû Uzel, Takahiro Tomoda +49 more

Papers

Driven by 33 papers — median percentile 91. Top paper: “International retrospective study of allogeneic hematopoietic cell transplantation for activated PI3K-delta syndrome”.

International retrospective study of allogeneic hematopoietic cell transplantation for activated PI3K-delta syndrome

Journal of Allergy and Clinical Immunology(2021)10.1016/j.jaci.2021.04.036

Top 9%

2.3DataRank

Top 9%72 citations

Zohreh Nademi, Maria Elena Maccari, Stephan Ehl, Gülbû Uzel, Takahiro Tomoda +49 more

Human type I IFN deficiency does not impair B cell response to SARS-CoV-2 mRNA vaccination

The Journal of Experimental Medicine(2022)10.1084/jem.20220258

N/A

1.3DataRank · unranked

47 citations

Paul Bastard, Pascal Chappert, Giovanna Barba–Spaeth, Slim Fourati, Alexis Vanderberghe +47 more

Effect of rituximab on immune status in children with mature B-cell non-Hodgkin lymphoma: a prespecified secondary analysis of the Inter-B-NHL Ritux 2010 trial

The Lancet Haematology(2023)10.1016/s2352-3026(23)00062-5

N/A

0.644DataRank · unranked

13 citations

Anne Aupérin, Simon Bomken, Monika Csóka, Bernarda Kazanowska, Aks Chiang +15 more

Partial RAG deficiency in humans induces dysregulated peripheral lymphocyte development and humoral tolerance defect with accumulation of T-bet+ B cells

Nature Immunology(2022)10.1038/s41590-022-01271-6

N/A

0.561DataRank · unranked

41 citations

Boglárka Ujházi, Péter Blazsó, José Luís Herrera, Christopher M. Tipton, Tomoki Kawai +45 more

Late-onset enteric virus infection associated with hepatitis (EVAH) in transplanted SCID patients

Journal of Allergy and Clinical Immunology(2023)10.1016/j.jaci.2022.12.822

N/A

0.425DataRank · unranked

16 citations

Jacques Fourgeaud, Julie Bruneau, Suk See De Ravin, Grace L. Smith, Mathieu Fusaro +53 more

Improved outcome of HSCT in STAT1 gain-of-function disease following JAK inhibition bridging

Journal of Human Immunity(2025)10.70962/jhi.20250027

N/A

0.373DataRank · unranked

11 citations

Mary Slatter, Juan Carlos Aldave Becerra, Laura Alonso, Erik G. J. von Asmuth, Safa Barış +38 more

On behalf of the SFGM‐TC: Real‐life use of third‐party virus‐specific T‐cell transfer in immunocompromised transplanted patients

HemaSphere(2024)10.1002/hem3.40

N/A

0.312DataRank · unranked

7 citations

Nadine Petitpain, Stéphane Morisset, Bénédicte Neven, Martin Castelle, Sarah Winter +40 more

Mutations disrupting the kinase domain of IKKα lead to immunodeficiency and immune dysregulation in humans

The Journal of Experimental Medicine(2024)10.1084/jem.20240843

N/A

0.208DataRank · unranked

3 citations

Boris Sorin, Charline Courteille, Duong Ho‐Nhat, Tom Le Voyer, J Debray +30 more

Single cell analysis of FOXP3 deficiencies in humans and mice unmasks intrinsic and extrinsic CD4 + T cell perturbations

bioRxiv (Cold Spring Harbor Laboratory)(2020)10.1101/2020.07.06.189589

N/A

0.123DataRank · unranked

1 citations

Louis‐Marie Charbonnier, Juliette Léon, Emmanuelle Six, Sevgi Keleş, Marianne Delville +15 more

Inherited human c-Rel deficiency disrupts myeloid and lymphoid immunity to multiple infectious agents

Journal of Clinical Investigation(2021)10.1172/jci150143

N/A

0DataRank · unranked

37 citations

David Langlais, Vivien Béziat, Franck Rapaport, Geetha Rao, Tomi Lazarov +42 more

Monoclonal antibody-mediated neutralization of SARS-CoV-2 in an IRF9-deficient child

Proceedings of the National Academy of Sciences(2021)10.1073/pnas.2114390118

N/A

0DataRank · unranked

34 citations

Peng Zhang, Paul Bastard, Karim Dorgham, Isabelle Melki, Alice Hadchouel +17 more

Monogenic early-onset lymphoproliferation and autoimmunity: Natural history of STAT3 gain-of-function syndrome

Journal of Allergy and Clinical Immunology(2022)10.1016/j.jaci.2022.09.002

N/A

0DataRank · unranked

128 citations

Tiphanie P. Vogel, Valentine G.J. Santarlas, Rahul Mhaskar, M.R. Smith, Alexandre F. Carisey +95 more

Human T-bet governs the generation of a distinct subset of CD11c high CD21 low B cells

Science Immunology(2022)10.1126/sciimmunol.abq3277

N/A

0DataRank · unranked

86 citations

Danielle T. Avery, Katherine Jackson, Masato Ogishi, Ibtihal Benhsaien, Likun Du +31 more

Vaccine breakthrough hypoxemic COVID-19 pneumonia in patients with auto-Abs neutralizing type I IFNs

Science Immunology(2022)10.1126/sciimmunol.abp8966

N/A

0DataRank · unranked

77 citations

Sara E. Vazquez, Jamin Liu, Matthew T. Laurie, Chung‐Yu Wang, Adrian Gervais +95 more

Human OTULIN haploinsufficiency impairs cell-intrinsic immunity to staphylococcal α-toxin

Science(2022)10.1126/science.abm6380

N/A

0DataRank · unranked

69 citations

Anna‐Lena Neehus, Emmanuel Laplantine, Frederik Staels, Masato Ogishi, Yoann Seeleuthner +57 more

The 2021 European Alliance of Associations for Rheumatology/American College of Rheumatology Points to Consider for Diagnosis and Management of Autoinflammatory Type I Interferonopathies: CANDLE/PRAAS, SAVI, and AGS

Arthritis & Rheumatology(2022)10.1002/art.42087

N/A

0DataRank · unranked

47 citations

Lovro Lamot, Micol Romano, Erkan Demirkaya, David Piskin, Sofia Torreggiani +27 more

Cutaneous barrier leakage and gut inflammation drive skin disease in Omenn syndrome

Journal of Allergy and Clinical Immunology(2020)10.1016/j.jaci.2020.04.005

N/A

0DataRank · unranked

29 citations

Elena Fontana, Kerry Dobbs, Veronica Marrella, Valentina Taverniti, Virginia Maina +30 more

Human CARMIL2 deficiency underlies a broader immunological and clinical phenotype than CD28 deficiency

The Journal of Experimental Medicine(2022)10.1084/jem.20220275

N/A

0DataRank · unranked

40 citations

Florian Gothe, Mana Momenilandi, Thomas Magg, Marie Materna, Philipp Peters +95 more

Inherited human ITK deficiency impairs IFN-γ immunity and underlies tuberculosis

The Journal of Experimental Medicine(2022)10.1084/jem.20220484

N/A

0DataRank · unranked

31 citations

Rui Yang, Rémy Rodriguez, Dominic P. Golec, Emmanuel Martin, Quentin Philippot +39 more

Hypomorphic RAG deficiency: impact of disease burden on survival and thymic recovery argues for early diagnosis and HSCT

Blood(2022)10.1182/blood.2022017667

N/A

0DataRank · unranked

30 citations

John R. Gerke, Markus J. Ege, Jolán E. Walter, Maaike Kusters, Austen Worth +36 more

STING Gain-of-Function Disrupts Lymph Node Organogenesis and Innate Lymphoid Cell Development in Mice

Cell Reports(2020)10.1016/j.celrep.2020.107771

N/A

0DataRank · unranked

34 citations

Carys A. Croft, Teresa L. Ai, Wei Qian, Amber M. Menos, Cathrine A. Miner +17 more

Vasculitis as a Major Morbidity Factor in Patients With Partial RAG Deficiency

Frontiers in Immunology(2020)10.3389/fimmu.2020.574738

N/A

0DataRank · unranked

16 citations

Jocelyn R. Farmer, Zsófia Földvári, Boglárka Ujházi, Jolanda Steininger, John W. Sleasman +20 more

Clinical, immunological features, treatments, and outcomes of autoimmune hemolytic anemia in patients with RAG deficiency

Blood Advances(2023)10.1182/bloodadvances.2023011264

N/A

0DataRank · unranked

2 citations

Bijun Sun, Kevin Y. Wu, Jocelyn R. Farmer, Boglárka Ujházi, Christoph B. Geier +29 more

IL-7–dependent and –independent lineages of IL-7R–dependent human T cells

Journal of Clinical Investigation(2024)10.1172/jci180251

N/A

0DataRank · unranked

7 citations

Masato Ogishi, Susanne Unger, Ottavia M. Delmonte, Julio César Orrego, Ahmad Yatim +65 more

Compound heterozygous mutations in the kinase domain of IKKα lead to immunodeficiency and immune dysregulation

medRxiv(2024)10.1101/2024.05.17.24307356

N/A

0DataRank · unranked

1 citations

Boris Sorin, Charline Courteille, Duong Ho‐Nhat, Tom Le Voyer, J Debray +28 more

Multiomics dissection of human RAG deficiency reveals distinctive patterns of immune dysregulation but a common inflammatory signature

Science Immunology(2025)10.1126/sciimmunol.adq1697

N/A

0DataRank · unranked

16 citations

Kerry Dobbs, Ottavia M. Delmonte, Andrew J. Martins, Francesca Pala, Tomoki Kawai +95 more

Clinical manifestations, disease penetrance, and treatment in individuals with SOCS1 insufficiency: a registry-based and population-based study

The Lancet Rheumatology(2025)10.1016/s2665-9913(24)00348-5

N/A

0DataRank · unranked

15 citations

Anna Franziska Wolfers, Oleg V. Borisov, Derek Hazard, Timothy Ronan Leahy, Marie Jeanpierre +51 more

β-Glucan–induced reprogramming of human macrophages inhibits NLRP3 inflammasome activation in cryopyrinopathies

Journal of Clinical Investigation(2020)10.1172/jci134778

N/A

0DataRank · unranked

76 citations

Mathieu Bohm, Alícia Corbellini Piffer, Rachel Lavenir, David L. Williams, Bénédicte Neven +4 more

A de novo dominant-negative PSMB8 mutation causes severe CANDLE/PRAAS due to arrested proteasome biogenesis

Annals of the Rheumatic Diseases(2025)10.1016/j.ard.2025.10.021

N/A

0DataRank · unranked

5 citations

Sara Alehashemi, Martin Wendlandt, Franziska G. Thiel, Adriana A. de Jesus, Jonas Johannes Papendorf +46 more

Factors associated with and kinetics of anti–IFN-α autoantibodies in RAG1/2 deficiency

Journal of Allergy and Clinical Immunology Global(2025)10.1016/j.jacig.2025.100521

N/A

0DataRank · unranked

0 citations

David Evan Potts, Bijun Sun, Marta Toth, Boglárka Ujházi, Svetlana Sharapova +49 more

Hematopoietic Cell Transplantation Cures Adenosine Deaminase 2 Deficiency: Report on 30 Patients

Journal of Clinical Immunology(2021)10.1007/s10875-021-01098-0

N/A

0DataRank · unranked

75 citations

Giorgia Bucciol, Seza Özen, Şule Ünal, İkbal Ok Bozkaya, Nurten Akarsu +46 more

Extended clinical and immunological phenotype and transplant outcome in CD27 and CD70 deficiency

Blood(2020)10.1182/blood.2020006738

N/A

0DataRank · unranked

100 citations

Sevgi Köstel Bal, Emily S.J. Edwards, Bethany Pillay, Raúl Jiménez Heredia, Funda Çipe +63 more

Preexisting autoantibodies to type I IFNs underlie critical COVID-19 pneumonia in patients with APS-1

The Journal of Experimental Medicine(2021)10.1084/jem.20210554

N/A

0DataRank · unranked

307 citations

Elizaveta Orlova, Leila Sozaeva, Romain Lévy, Alyssa James, Monica M. Schmitt +60 more

Bénédicte Neven

Indexed papers

Top data-sharing exemplar

Papers