Hemanth R. Nelvagal

Also affiliated with National Hospital for Neurology and Neurosurgery, Research Network (United States), University College London

MedicineBiochemistry, Genetics and Molecular Biology

Pilot corpus only

This score is computed over theSindex pilot corpus and does not cover the full scientific literature. Scores are relative to papers we have ingested — papers, authors, and institutions outside the pilot are not represented. Methodology.

Top 100%percentile

0Author DataRank

Indexed papers

0in pilot corpus

datarank_citation_only_1hop_v6· scope data_onlyMethodology

Papers

Driven by 17 papers. Top paper: “Intracranial delivery of AAV9 gene therapy partially prevents retinal degeneration and visual deficits in CLN6-Batten disease mice”.

Intracranial delivery of AAV9 gene therapy partially prevents retinal degeneration and visual deficits in CLN6-Batten disease mice

Molecular Therapy — Methods & Clinical Development(2021)10.1016/j.omtm.2020.12.014

N/A

0.449DataRank · unranked

19 citations

Hemanth R. Nelvagal, Timothy A. Poole, Bin Lü, Tyler B. Johnson, Samantha S. Davis +10 more

Cross-species efficacy of enzyme replacement therapy for CLN1 disease in mice and sheep

Journal of Clinical Investigation(2022)10.1172/jci163107

N/A

0.449DataRank · unranked

19 citations

Samantha L. Eaton, Sophie H. Wang, Elizabeth M. Eultgen, Keigo Takahashi, Steven Q. Le +25 more

Tralesinidase Alfa Enzyme Replacement Therapy Prevents Disease Manifestations in a Canine Model of Mucopolysaccharidosis Type IIIB

Journal of Pharmacology and Experimental Therapeutics(2022)10.1124/jpet.122.001119

N/A

0.339DataRank · unranked

7 citations

Bethann Valentine, Andrew S. Hess, Jackie K. Jens, Elizabeth Snella, Maryam Jamil +32 more

Recombinant NAGLU-IGF2 prevents physical and neurological disease and improves survival in Sanfilippo B syndrome

bioRxiv (Cold Spring Harbor Laboratory)(2021)10.1101/2021.08.06.455469

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0DataRank · unranked

1 citations

Shih‐hsin Kan, Marie S. Roberts, Joshua T. Dearborn, Rui Wang, Shan Li +15 more

Effects of chronic cannabidiol in a mouse model of naturally occurring neuroinflammation, neurodegeneration, and spontaneous seizures

Scientific Reports(2022)10.1038/s41598-022-15134-5

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0DataRank · unranked

25 citations

Hemanth R. Nelvagal, Nicholas Rensing, Keigo Takahashi, Stephanie M. Hughes, Thomas M. Wishart +4 more

Glial Dysfunction and Its Contribution to the Pathogenesis of the Neuronal Ceroid Lipofuscinoses

Frontiers in Neurology(2022)10.3389/fneur.2022.886567

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0DataRank · unranked

23 citations

Hemanth R. Nelvagal, Jenny Lange, Jonathan D. Cooper, Keigo Takahashi

Effects of chronic cannabidiol in a mouse model of naturally occurring neuroinflammation, neurodegeneration, and spontaneous seizures

bioRxiv (Cold Spring Harbor Laboratory)(2022)10.1101/2022.03.07.483344

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0DataRank · unranked

1 citations

Hemanth R. Nelvagal, Nicholas Rensing, Stephanie M. Hughes, Thomas M. Wishart, Jonathan D. Cooper +3 more

Cortical interneuron loss and seizure generation as novel clinically relevant disease phenotypes in Cln2 R207X mice

bioRxiv (Cold Spring Harbor Laboratory)(2022)10.1101/2022.03.11.483984

N/A

0DataRank · unranked

0 citations

Elizabeth M. Eultgen, Sophie H. Wang, Nicholas Rensing, Hemanth R. Nelvagal, Joshua T. Dearborn +4 more

Neuronal deletion of the circadian clock gene Bmal1 induces cell-autonomous dopaminergic neurodegeneration

JCI Insight(2023)10.1172/jci.insight.162771

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0DataRank · unranked

29 citations

Patrick W. Sheehan, Jessica N. Haines, P. Gómez, Adya Dhuler, Collin J. Nadarajah +9 more

Gene therapy ameliorates spontaneous seizures associated with cortical neuron loss in a Cln2R207X mouse model

Journal of Clinical Investigation(2023)10.1172/jci165908

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0DataRank · unranked

18 citations

Elizabeth M. Eultgen, Sophie H. Wang, Nicholas Rensing, Hemanth R. Nelvagal, Joshua T. Dearborn +6 more

Bowel dysmotility and enteric neuron degeneration in lysosomal storage disease mice is prevented by gene therapy

bioRxiv (Cold Spring Harbor Laboratory)(2023)10.1101/2023.05.26.542524

N/A

0DataRank · unranked

2 citations

Letitia L. Williams, Sophie H. Wang, Elizabeth M. Eultgen, Keigo Takahashi, Hemanth R. Nelvagal +12 more

GABAergic interneurons contribute to the fatal seizure phenotype of CLN2 disease mice

bioRxiv (Cold Spring Harbor Laboratory)(2024)10.1101/2024.03.29.587276

N/A

0DataRank · unranked

0 citations

Nicholas Rensing, Elizabeth M. Eultgen, Sophie H. Wang, Hemanth R. Nelvagal, Steven Q. Le +8 more

Gene therapy ameliorates bowel dysmotility and enteric neuron degeneration and extends survival in lysosomal storage disorder mouse models

Science Translational Medicine(2025)10.1126/scitranslmed.adj1445

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0DataRank · unranked

17 citations

Matthew J. Jansen, Letitia L. Williams, Sophie H. Wang, Elizabeth M. Eultgen, Keigo Takahashi +17 more

Comparative proteomic profiling reveals mechanisms for early spinal cord vulnerability in CLN1 disease

Scientific Reports(2020)10.1038/s41598-020-72075-7

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0DataRank · unranked

15 citations

Maica Llavero Hurtado, Samantha L. Eaton, Rachel Kline, Douglas J. Lamont, Mark S. Sands +3 more

Limited therapeutic efficacy of N-acetyl-L-leucine in a mouse model of CLN1 disease

Scientific Reports(2025)10.1038/s41598-025-32984-x

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0DataRank · unranked

0 citations

Nicole A. Pagán Torres, Hsintsung Chen, Letitia L. Williams, Elizabeth M. Eultgen, Agnieszka Nowacka +6 more

Spinal manifestations of CLN1 disease start during the early postnatal period

Neuropathology and Applied Neurobiology(2020)10.1111/nan.12658

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0DataRank · unranked

27 citations

Joshua T. Dearborn, John R. Østergaard, Mark S. Sands, Jonathan D. Cooper, Hemanth R. Nelvagal

Substrate reduction therapy for Krabbe disease and metachromatic leukodystrophy using a novel ceramide galactosyltransferase inhibitor

Scientific Reports(2021)10.1038/s41598-021-93601-1

N/A

0DataRank · unranked

19 citations

Christina R. Mikulka, Bing Wang, Sanjay Chandriani, Sundeep Chandra, Yue Xu +14 more